Order NO. D261236
产品描述
概述
This gene encodes a member of a family of proteins containing several distinct regions, including a metalloproteinase domain, a disintegrin-like domain, and a thrombospondin type 1 (TS) motif. The enzyme encoded by this gene specifically cleaves von Willebrand Factor (vWF). Defects in this gene are associated with thrombotic thrombocytopenic purpura. Alternative splicing results in multiple transcript variants.
应用
酶联免疫吸附测定(ELISA),免疫组织化学(IHC)
属性
保存缓冲液 |
-20°C, pH7.4 PBS, 0.05% NaN3, 40% Glycerol
|
运输条件 |
2-8°C
|
靶点 Uniprot 登记号 |
Q76LX8
|
靶点基因 ID |
11093
|
靶点全称 |
ADAM metallopeptidase with thrombospondin type 1 motif, 13
|
靶点别名 |
VWFCP; C9orf8; vWF-CP; ADAM-TS13; ADAMTS-13
|
靶点研究领域 |
Signal Transduction, Cell Biology
|
亚型 |
Immunogen-specific rabbit IgG
|